W Chen, L Fu, T Zhang, L Liu

Abstract

Introduction: Ovarian sex cord tumours with annular tubules (SCTAT) is extremely rare in children with Peutz-Jeghers syndrome (PJS). We reported a case of ovarian SCTAT in a girl with PJS and reviewed the literature. Case presentation: A 13-year-old girl PJS was admitted for menorrhagia during the last 1.5 years, accompanied by intermittent abdominal pain and a 2-day history of pallor. Ultrasound and computerised tomography showed bilateral ovarian tumours. Surgical resection was performed, and the patient was diagnosed as bilateral ovarian SCTAT. The patient had an uneventful follow-up. Conclusion: Fertility-sparing tumour resection is feasible for ovarian SCTAT in children with PJS. Long-term follow-up is mandatory for the postoperative patients.